Menkes disease: report of two cases.

نویسندگان

  • F Alan Walker
  • Curt Goho
  • Robert B Schanzer
چکیده

Menkes disease is a rare, autosomal recessive disorder characterized by neuronal degeneration, abnormal hair, malformed connective tissue, mental retardation, and a life span of three years. Previously reported dental findings include a high arched palate, delayed eruption of secondary dentition, and open bite. The case of twin seven-year-old males with Menkes disease is presented, along with previously unreported dental findings of spindle-shaped root resorption patterns on the primary maxillary central and lateral incisors.

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عنوان ژورنال:
  • ASDC journal of dentistry for children

دوره 69 1  شماره 

صفحات  -

تاریخ انتشار 2002